Sesión Anatomoclínica I-2018 Autopsia No 38190,Femenina de 57 años con infertilidad primaria, fibrosis pleural y enfermedad renal crónica estadio V secundaria a fibrosis retroperitoneal por enfermedad relacionada con IgG4.

 

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Auteurs: Salazar Arias, Nazareth, Gaitán Brenes, Gustavo, Fuentes Alfaro, Fabiola, Quesada Aguilar, Carlos, Jiménez Montero, Ernesto
Format: artículo original
Statut:Versión publicada
Date de publication:2019
Description:A case of a 57-year-old female patient, with history of primary infertility, chronic kidney disease (CKD) stage V secondary to obstructive uropathy; in whom, weight loss studies documented metastasis of poorly differentiated adenocarcinoma without identifying its origin in a retroperitoneal biopsy. The patient evolved insidiously in the course of 16 years. Subsequently, she consulted for progressive dyspnea. Pleural fibrosis and persistently elevated erythrocyte sedimentation rate over the years was documented. The patient progressed to acuterespiratory failure, hydropic decompensation and died. The autopsy showed compatible findings with retroperitoneal fibrosis due to IgG4-related disease
Pays:Portal de Revistas UCR
Institution:Universidad de Costa Rica
Repositorio:Portal de Revistas UCR
Langue:Español
OAI Identifier:oai:archivo.portal.ucr.ac.cr:article/37327
Accès en ligne:https://archivo.revistas.ucr.ac.cr/index.php/clinica/article/view/37327